Successful aortic reimplantation in a three-year-old child with Marfan syndrome.

نویسندگان

  • Yoshinori Miyahara
  • Shingo Kasahara
  • Masami Takagaki
  • Shunji Sano
چکیده

Aortic root dilatation is rare in children, and is often secondary to Marfan syndrome (MFS). We experienced a case of a three-year-old boy (92 cm, 12 kg) with MFS presenting with progressive dilatation of aortic root. We electively performed a valve-sparing aortic root replacement using a 24-mm Gelweave Valsalva graft. Although the patient required a mitral valve repair due to infective endocarditis postoperatively, the recovery from the second surgery was uneventful. This case is one of the youngest children of valve-sparing aortic root replacement in the literature.

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عنوان ژورنال:
  • Interactive cardiovascular and thoracic surgery

دوره 11 2  شماره 

صفحات  -

تاریخ انتشار 2010